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Table 1 Clinical characteristics of postmortem cases

From: SGTA associates with intracellular aggregates in neurodegenerative diseases

Disease

Case number

Age at death (years)

Sex (M/F)

Disease duration (months)

SGTA-reactive inclusions

SCA1

1

55

F

144

Positive

SCA1

2

71

F

492

Positive

SCA2

3

57

M

120

Positive

SCA2

4

48

F

252

Positive

SCA3

5

40

F

156

Positive

SCA3

6

51

F

240

Negative

SCA3

7

36

M

168

Positive

DRPLA

8

46

F

131

Positive

PD

9

82

F

155

Negative

PD

10

94

F

324

Negative

PD

11

82

F

66

Negative

PD

12

58

F

228

Negative

MSA

13

48

M

85

Positive

MSA

14

75

M

84

Positive

MSA

15

65

F

40

Positive

MSA

16

79

F

48

Positive

ALS

17

69

F

7

Negative

ALS

18

64

M

36

Negative

ALS

19

87

M

29

Negative

ALS

20

61

M

9

Negative

ALS

21

75

F

7

Negative

ALS

22

72

M

20

Negative

  1. M male, F female, SCA spinocerebellar ataxia, DRPLA dentatorubral–pallidoluysian atrophy, PD Parkinson’s disease, MSA multiple system atrophy, ALS amyotrophic lateral sclerosis